Dravet syndrome is a rare type of epilepsy and severe. The "severe myoclonic epilepsy in infancy" was described for the first time by Charlotte Dravet in 1978 in Marseille. Common characteristics have been observed: beginning in the first year of life, sensitivity to fever, various types of seizures, including myoclonic, and mental retardation. The following descriptions are then led to the recognition of a true epileptic syndrome. Renzo Guerrini contribute to the understanding of genetic factors and response to antiepileptic drugs. New molecules have emerged since, and studies on cognitive impairment have identified developmental delay. The authors offer a synthesis of Dravet syndrome, including a description of electro-clinical features, which help to better diagnosis. The different therapeutic options are illustrated in the book, which also updates the knowledge of genetics. Although many questions remain in understanding this syndrome, this monograph is a valuable tool for medical practitioners to better care for children with epilepsy.